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Letterer-Siwe disease

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Location: http://chorus.rad.mcw.edu/doc/00230.html

Description: Acute diseminated form of histiocytosis X
* age 0 - 1 yr
* worst prognosis (70% mortality)
* visceral involvement: hepatosplenomegaly
* purpura, anemia, lymphadenopathy
* bone: extensive lytic skull lesions, "raindrop" skull

Type: Reference Material
Author/Contact: Charles E. Kahn, Jr., MD
Institution: CHORUS
Primary Subject/Category:

Language: English

Submitted by: admin
Hits: 1232
Added: Thu Jan 31 2002
Last Modified: Mon Jul 27 2009