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Osteopoikilosis Diseases Database

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Location: http://www.diseasesdatabase.com/ddb30071.htm

Description: "An asymptomatic, autosomal dominant trait in which pea-sized sclerotic spots, prominent in the metaphyseal area, are accompanied by unique cutaneous lesions. These are yellowish papules or plaques with increased elastin content. (From Cecil Textbook of Medicine, 19th ed, pp1434-35)" aka/or Buschke-Ollendorf syndrome aka/or Dermatofibrosis lenticularis aka/or Disseminated dermatofibrosis aka/or Osteodermatopoikilosis aka/or Osteopathia condensans disseminata may cause or feature X-ray abnormalities Osteosclerosis may be a risk factor for Benign neoplastic conditions Connective tissue nevus of skin may be allelic with Melorheostosis belong(s) to the category of Autosomal dominant conditions

Type: Reference Material
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Institution: Diseases Database
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Language: English

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Added: Sun Dec 17 2006