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Mafucci syndrome CHORUS

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Location: http://chorus.rad.mcw.edu/doc/00241.html

Description: * rare
* multiple enchondromata
o 40 - 45% malignant transformation --> chondrosarcoma
* multiple cavernous hemangiomata
o may degenerate --> angiosarcoma

Type: Reference Material
Author/Contact: Charles E. Kahn, Jr., MD
Institution: CHORUS
Primary Subject/Category:

Language: English

Submitted by: admin
Hits: 1246
Added: Thu Jan 31 2002
Last Modified: Tue Jul 28 2009