Osteofibrous Dysplasia eMedicine Orthopedics

Description: Osteofibrous dysplasia is a rare condition that most commonly affects the tibia (see Image 1). Osteofibrous dysplasia is a nonneoplastic lesion that is frequently asymptomatic and has an unknown etiology. Most lesions of osteofibrous dysplasia affect the cortex of the tibia, predominantly the middle third of the diaphysis. The cortex often is expanded and thinned with multiple radiolucencies mixed with intervening areas of sclerosis. The second most common site of involvement is the fibula.
Synonyms and related keywords: ossifying fibroma, congenital fibrous dysplasia, congenital fibrous defect of the tibia, intracortical fibrous dysplasia, infantile pseudarthrosis of the tibia, localized osteitis fibrosa, congenital kyphoscoliotic tibia, congenital pseudarthrosis, Campanacci syndrome, Campanacci's syndrome
Letts & Davidson 2005