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Polyostotic Fibrous Dysplasia DiseasesDatabase
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Location: http://www.diseasesdatabase.com/ddb7880.htm
Description: Osteitis Fibrosa Disseminata:
"A disease of bone marked by thinning of the cortex and replacement of bone marrow by gritty fibrous tissue containing bony spicules, producing pain, disability, and gradually increasing deformity. Only one bone may be involved (FIBROUS DYSPLASIA, MONOSTOTIC) or several (FIBROUS DYSPLASIA, POLYOSTOTIC). (From Dorland, 28th ed)"
2 synonyms or equivalents were found.
Polyostotic fibrous dysplasia
aka/or
McCune-Albright syndrome
may cause or feature Miscellaneous syndromes
Bone lysis
Hyperostosis
Pathological fracture
Symptoms and Signs
Café au lait spots
Facies abnormality
Precocious puberty
X-ray abnormalities
Erlenmeyer flask deformity
Endocrine conditions
Cushing's syndrome
Hyperthyroidism
Inflammatory conditions
Osteitis
may be a risk factor for Endocrine conditions
Pituitary tumour (growth hormone secreting)
Neoplastic conditions
Phaeochromocytoma
Type: Reference Material
Author/Contact: Not available
Institution: DiseasesDatabase
Primary Subject/Category:
Language: English
Submitted by: admin
Hits: 883
Added: Sat Dec 09 2006