Escobar Syndrome Associated with Thoracic Kyphoscoliosis Lordoscoliosis and Severe Restrictive Lung Disease

Description: Escobar syndrome or multiple pterygium syndrome is characterized by a web across every flexion crease in the extremities, most notably the popliteal space. In addition, this syndrome is associated with two other structural anomalies: a vertical talus and congenital lordoscoliosis. We present a case report of a patient with Escobar syndrome who was initially managed conservatively and subsequently had severe and debilitating progression and respiratory decompensation ultimately requiring surgical intervention.
Escobar syndrome (multiple pterygium syndrome) associated with thoracic kyphoscoliosis, lordoscoliosis, and severe restrictive lung disease: a case report. Dodson CC, Boachie-Adjei O. HSS J. 2005 Sep;1(1):35-9.