Streeter Dysplasia eMedicine Orthopedics

Description: Streeter dysplasia is a term used to describe a complex disorder characterized by constricting rings, acrosyndactyly, or, often, amputations of the extremities of neonates. It is analogous to constriction band or amniotic band syndrome (ABS), which was recognized as early as 300 BC. Hippocrates suggested that extrinsic pressures from a ruptured amniotic membrane lead to the formation of bands or digital amputations. In 1652, J.B. van Helmont reported on intrauterine amputations, which he attributed to the pregnant mothers having looked upon maimed soldiers. Montgomery in 1832 and Simpson in 1836 subsequently described series of amniotic band–associated deformities and discussed the differences between agenesis- and amniotic band–induced amputations.
Synonyms and related keywords: congenital constriction band syndrome, amniotic band syndrome, ABS, constricting rings, acrosyndactyly, intrauterine amputation, digital amputations, ADAM complex, limb body wall syndrome, pseudo-ainhum, pseudoainhum, hemihypertrophy, anterolateral bowing, pseudarthrosis, leg-length discrepancy, teratologic clubfeet
Twee Do, MD 2006