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2006 Severe scoliosis associated with Costello syndrome
J Orthop Surg (Hong Kong). 2006 Dec;14(3):346-9.
Severe scoliosis associated with Costello syndrome: a case report.Motosuneya T, Asazuma T, Tsuji T, Watanabe H, Nakayama Y, Nemoto K.
Department of Orthopaedic Surgery, National Defense Medical College, Namiki, Tokorozawa, Saitama, Japan.
Costello syndrome is characterised by dwarfism, unique cutaneous lesions, a distinct facial gestalt, and mental retardation. There have been no detailed reports of severe spinal deformities requiring surgical treatment as a complication of Costello syndrome. We report a case of a 10-year-old girl with progressive scoliosis associated with Costello syndrome. She underwent anterior release and posterior surgical correction and fusion from T5 to L2 using a third generation hook and rod system plus spinous process wiring. Congenital portal vein deficiency and coagulopathy were other major complications. At 15-month follow-up, the patient had good balance and no evidence of instrumentation failure.
Type: Case Study
Author/Contact: Motosuneya et al
Submitted by: admin
Added: Sat Jul 28 2007