MHE MedPix

Description: Multiple heredity exostosis is characterized by palpable osseous projections from the cortex of the bone, joint restrictions, and secondary osseous deformities. Deformities that are frequently noted include widening of the proximal femoral metaphysis, bilateral coxa valga, deviation and shortening of the ulna, and forearm shortening. This disorder is autosomal dominant and is seen in the first or second decade of life. It is distinguished from osteochondroma by its multiplicity. Greater than one hundred protuberances may be present and they are commonly symmetric. Complications include vascular injury, neurologic compromise, bursa formation, pathologic fracture and malignant transformation.