cleidocranial dysplasia dysostosis Wheeless

Description: Discussion: - autosomal dominant proportionate dwarfism that affects bones formed intramembranously (eg. facial bones, cranium, & clavicles); - dislocations of hips, knees, and the radial heads may occur; - clavicle: - most commlonly, absence of the central portion of the clavicle with rudimentary medial and lateral portions remaining; - may be confused w/ pseurdoarthrosis of the clavicle - coxa vara: - consider intertrochanteric osteotomy if varus is <100 deg;