OWL: OCOSH Classification/Bone Diseases/Bone Developmental Diseases/Osteochondrodysplasia/Fibrous Dysplasia of Bone/Monostotic Fibrous Dysplasia

Fibrous dysplasia

Endres & Wilke — 2009-01-11 23:05:51 GMT

Differential diagnosis of cystic lesions in the proximal femur: a case report Stefan Endres and Axel Wilke Cases Journal 2009, 2:26 (full text available)
We are reporting about the case of a 22-year old woman, who made a first visit as an outpatient with pain that arose in acute form in the area of the left groin. The patient history did not indicate a preceding trauma, or an inflammatory or malignant disease.

Jaffe Lichtenstein monostotic fibrous dysplasia of bone

2006-12-09 23:05:51 GMT

Jaffe-Lichtenstein monostotic fibrous dysplasia of bone: Definition(s) via UMLS "A disease of bone marked by thinning of the cortex and replacement of bone marrow by gritty fibrous tissue containing bony spicules, producing pain, disability, and gradually increasing deformity. Only one bone may be involved (FIBROUS DYSPLASIA, MONOSTOTIC) or several (FIBROUS DYSPLASIA, POLYOSTOTIC). (From Dorland, 28th ed)" 2 synonyms or equivalents were found. Jaffe-Lichtenstein monostotic fibrous dysplasia of bone aka/or Monostotic osteitis fibrosa may cause or feature + Symptoms and Signs Caf� au lait spots Facies abnormality X-ray abnormalities Intracranial calcification Osteosclerosis Inflammatory conditions Osteitis

Jaffe Lichtenstein Syndrome

2006-12-09 23:05:51 GMT

Description: A monostotic form of fibrous dysplasia of bone. Constitutional, benign disease of the bones characterised by excessive proliferation of single or multiple circumscribed fibrous lesions, predominantly in the long bones, which predispose to painful bone deformities and pathological fractures, limping, unequal limp length, skull asymmetry, leontiaslike appearance, scoliosis, lordosis, and chest deformity. Irregular macular dermal pigmentation is a variable feature. Onset usually during first two decades of life. Aetiology unknown. No fever; characteristic X-ray. The disorder is usually sporadic, but familial cases have been reported. Also known as: Jaffe�s syndrome II Jaffe-Lichtenstein dysplasia Jaffe-Lichtenstein fibrous dysplasia Jaffe-Lichtenstein-Uehlinger syndrome McCune-Albright syndrome

Monostotic Fibrous Dysplasia Pathweb

2006-12-09 23:05:51 GMT

High power view of monostotic fibrous dysplasia of bone �A high power view of a focus of new bone formation in a fibrous dysplasia of bone. �The spicule of bone looks structurally normal, with a normal dense osteoid matrix, and lacunea that contain osteocytes. �Surrounding the fragment of new bone formation is a fibrous matrix containing numerous active fibroblasts. (Description By:T.V.Rajan, M.D. ) (Image Contrib. by:T.V.Rajan, M.D. UCHC )

Monostotic Fibrous Dysplasia TumorLibrary

James Johnston — 2010-06-07 23:05:51 GMT

Illustrated cases. See also - Fibrous dysplasia with secondary osteosarcoma