Basal Cell Nevus (Subscribe)

Basal cell nevus syndrome is an autosomal dominant condition with complete penetrance and variable expressivity. It is characterized by five major components, including multiple nevoid basal cell carcinomas, jaw cysts, congenital skeletal abnormalities, ectopic calcifications, and plantar or palmar pits. Other features include a host of benign tumors, ocular defects, and cleft lip and palate. Guidelines for diagnosis include a family history, careful oral and skin examinations, chest and skull ...

Basal Cell Nevus Syndrome BCNS NEVOID BASAL CELL CARCINOMA SYNDROME; NBCCS MULTIPLE BASAL CELL NEVI, ODONTOGENIC KERATOCYSTS, AND SKELETAL ANOMALIES FIFTH PHACOMATOSIS GORLIN SYNDROME GORLIN-GOLTZ SYNDROME HYDROCEPHALUS, COSTOVERTEBRAL DYSPLASIA, AND SPRENGEL ANOMALY, INCLUDED

Introduction Clinical Differentials Workup Treatment Follow-up Pictures Bibliography Author: Daniel Berg, MD, Program Director of Dermatologic Surgery, Associate Professor, Department of Internal Medicine, Division of Dermatology, University of Washington 2005

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