Contracture (Subscribe)  

Extensive notes on -
Contractures with neuromuscular disorders
Arthrogryposis
Bethlem Myopathy
Congenital muscular dystrophy
Dermatomyositis
Dystrophinopathies
Emery-Dreifuss
Fasciitis
Hereditary IBM with ophthalmoplegia
IM drug injections
Nemaline (Rod) myopathy: Severe
Rigid spine syndromes
Scleroatonic muscular dystrophy (Ullrich)
Spinal Muscular Atrophy
* 5q-linked Congenital
* X-linked Infantile
Tel Hashomer camptodactyly
Williams-Beuren syndrome
Joint Hyperlaxity
Ullrich CMD
CMD + Joint hyperlaxity
Mental retardation

Escobar syndrome or multiple pterygium syndrome is characterized by a web across every flexion crease in the extremities, most notably the popliteal space. In addition, this syndrome is associated with two other structural anomalies: a vertical talus and congenital lordoscoliosis. We present a case report of a patient with Escobar...

Children with neuromuscular disorders often manifest fixed knee flexion deformity due to muscle weakness or imbalance. They tend to develop a crouch gait pattern that may prove refractory to physical therapy, bracing, or spasticity management (Botox/baclofen); for those children, surgical management may be indicated. In addition to hamstring recession for...

Illustration of exercises. Wheeless' Textbook of Orthopaedics

Knee Flexion Contractures: Soft Tissue Correction With Monolateral External Fixation from Journal of the Southern Orthopedic Association James F. Mooney III, MD, L. Andrew Koman, MD, Winston-Salem, NC Abstract We assessed the efficacy of progressive soft tissue distraction using monolateral external fixation in the management of severe knee flexion contractures. We prospectively evaluated 10...

Knee flexion deformity can cause marked physical disability. Acute correction, whether nonoperative or operative, may lead to serious complications. We treated 50 patients (71 knees) between 1994 and 2002 with the Ilizarov external fixator. The deformity was gradually corrected using Ilizarov principles.
Gamal Ahmed Hosny, MD1 and Mohamed Fadel, MD Clin...

OBJECTIVE. Our purpose was to describe the use of MR imaging in the evaluation of the positions of the popliteal artery and peroneal nerve in children with popliteal pterygium syndrome for preoperative planning and to describe the typical appearance of popliteal pterygium on MR imaging.
CONCLUSION. By depicting the popliteal artery...

The images show a boy with webbing or pterygia in the cubital, popliteal and neck areas. This is multiple pterygia syndrome, also know as Escobar's Syndrome. It is a rare congenital disorder with sporadic or autosomal recessive inhertance. An autosomal dominant form has also been reported.
Features include multiple joint contractures...

Diagnostic, prognostic and genetic features. Not much about treatment.

The multiple pterygium syndrome is a rare autosomal recessive condition characterised by arthrogryposis multiplex congenita, pterygia of the neck, fingers, and antecubital, popliteal, and intercrural areas, growth retardation, and facial, vertebral, and genital anomalies. We present two unrelated patients of 17 and 6 years of age, respectively, affected with this...

Popliteal Pterygium syndrome is characterized by the presence of web, which may extend from heel to ischial tuberocity. There is also associated short sciatic nerve and other fascial and genitourinary findings because of which it is also known as Fascio-Genito-Popliteal syndrome.
Gupta M, Jora R. Indian Pediatr. 2006 May;43(5):450-1.

Pterygium syndrome is a complex and rare congenital deformity that consists of contractures involving multiple flexural surfaces and associated craniofacial anomalies. It often has associated conditions, including anomalies of the cardiovascular, respiratory, gastrointestinal and genitourinary systems. It may present in different forms, including multiple pterygium syndrome of Escobar, lethal multiple...

This article is primarily about the treatment of the orofacial feature (cleft lip and palate). It mentions that popliteal pterygium is associated with this condition. Symptoms of van der Woude syndrome have been seen in individuals with popliteal pterygium syndrome, which has also been linked to mutations in the same...