Diastomatomyelia

Description: Clinical presentation: 6 month girl born with spastic paraplegia and dislocation of the right hip. Anal sphincter, poor tone. There was skin pigmentation over the lower lumbar spine, posteriorly.
There is a scoliosis with the point of maximal curvature at the level of the lowest thoracic vertebrae. There is a widened interpedicular distance at the same level. A curvilinear bone density is projected in the mid-line at the level of presumptive 11th and 12th thoracic vertebrae. There appears to be a defect in the posterior structures of the lowest visible lumbar vertebra.