Proximal Femoral Focal Deficiency eMedicine Orthopedics

Description: Author: Michael G Dennis, MD 2008
Proximal femoral focal deficiency (PFFD) is an uncommon but complex problem. PFFD was commonly grouped with other disorders, such as coxa vara and short bowed femurs, which led to confusion and misunderstanding.
In general, in individuals with PFFD, the proximal femur is partially absent, and the entire limb is overall shortened. A few main biomechanical abnormalities are present in children with PFFD, as well as in adults with limb deficiencies. These include limb length discrepancies, malrotation, proximal joint instability, and inadequacy of the proximal musculature.
Synonyms and related keywords: PFFD, absent proximal femur, knee arthrodeses, foot amputation, Van Nes rotationplasty, limb rotationplasty, hip reconstruction, hip stabilization, limb lengthening, iliofemoral arthrodesis