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1989 Scoliosis in neurofibromatosis
J Bone Joint Surg Br. 1989 Mar;71(2):246-51.
Scoliosis in neurofibromatosis. The natural history with and without operation.Calvert PT, Edgar MA, Webb PJ.
Royal National Orthopaedic Hospital, Stanmore, Middlesex, England.
We reviewed 47 patients with neurofibromatosis and dystrophic spinal deformities; 32 of these patients had been untreated for an average of 3.6 years and in them the natural history was studied. The commonest pattern of deformity at the time of presentation was a short angular thoracic scoliosis, but with progression the angle of kyphosis also increased. Deterioration during childhood was usual but its rate was variable. Severe dystrophic changes in the apical vertebrae and in particular anterior scalloping have a poor prognosis for deterioration. The dystrophic spinal deformity of neurofibromatosis requires early surgical stabilisation which should be by combined anterior and posterior fusion if there is an abnormal angle of kyphosis or severely dystrophic apical vertebrae. Some carefully selected patients can be treated by posterior fusion and instrumentation alone.
Type: Reference Material
Author/Contact: Calvert et al
Institution: JBJS B
Submitted by: admin
Added: Sat Jul 28 2007