Jaffe Lichtenstein Syndrome

Description: Description: A monostotic form of fibrous dysplasia of bone. Constitutional, benign disease of the bones characterised by excessive proliferation of single or multiple circumscribed fibrous lesions, predominantly in the long bones, which predispose to painful bone deformities and pathological fractures, limping, unequal limp length, skull asymmetry, leontiaslike appearance, scoliosis, lordosis, and chest deformity. Irregular macular dermal pigmentation is a variable feature. Onset usually during first two decades of life. Aetiology unknown. No fever; characteristic X-ray. The disorder is usually sporadic, but familial cases have been reported. Also known as: Jaffe’s syndrome II Jaffe-Lichtenstein dysplasia Jaffe-Lichtenstein fibrous dysplasia Jaffe-Lichtenstein-Uehlinger syndrome McCune-Albright syndrome